Perioperative anesthetic management in a child with Beckwith-Wiedman syndrome

Beckwith-Wiedemann Syndrome (BWS), a rare genetic disorder, poses distinctive challenges
for anesthesiologists due to its associated physical anomalies and potential complications. This
case report details the anesthetic management of a 2-year-old boy with BWS undergoing a
procedure for agenesis testis bilateral. Key considerations include macrosomia, hypoglycemia
risk, airway abnormalities, cardiovascular anomalies, and abdominal wall defects. The patient
successful perioperative care involved meticulous preoperative assessment, careful planning,
and collaboration with specialized medical teams. Anesthesia comprised a combination of
medications, monitoring, and airway management techniques tailored to the patient’s unique
needs. The discussion emphasizes the importance of considering macrosomia, hypoglycemia,
anatomical abnormalities, and other factors in anesthesia planning for BWS patients. Vigilant
postoperative monitoring is highlighted. The conclusion underscores the necessity for
experienced anesthesiologists familiar with the challenges associated with BWS, emphasizing
the significance of tailored approaches, comprehensive assessments, and collaborative care for
the safety and well-being of these patients during surgical interventions.