Primary Retroperitoneal Mucinous Cystadenoma Emerging from the Retrorectal Space in A Male Patient - A Case Report

Karagjozov, Aleksandar and Petrushevska, G. and Milev, Ilija (2013) Primary Retroperitoneal Mucinous Cystadenoma Emerging from the Retrorectal Space in A Male Patient - A Case Report. Physioacta. Journal of Macedonian Association of Physiologists and Anthropologista, 7 (2). pp. 85-93. ISSN 1857-5587


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The paper presents a rare and according to our knowledge a unique case in the world literature of a primary retroperitoneal mucinous cystadenoma (PRMC) with borderline malignancy in a male patient with localization in the retrorectal space, presented in a form of a system of perianal fistulas. The patient is a 67-year-old male, with a 23-year-old history of perianal fistula, which in the past two years has progressed by forming several severe fistulous channels on both sides of the anus and gluteal regions from which there was gross secretion of a mucinous content. He was operated on the assumption that the gross mucoproduction is from the rectal mucosa. In the first part of the operation, which was carried out in a jackknife position with epidural anesthesia, all the perianal and gluteal mucoid masses along with part of the muscle tissue and superficial fascia were removed creating a big defect. When it was obvious that the mucoid masses are emerging deeply from the praesacrococcygeal – retrorectal space, the patient was put in gynecological position with general anesthesia, and cylindric amputation of the rectum according to Milles – Thompson, with removing of all of the tumorous tissue, was performed. During the final stage, the perineal wound was closed by rotating and sliding skin flaps. Postoperatively, there was a minor skin dehiscence on the perineal wound that healed spontaneously, and now four months after the operation, the patient is well, grateful, and without signs of local recidivism. PRMC is extremely rare entity of only about 50 cases reported in the world literature and most of them in female patients. Our case will be overall 4-th reported case of PRMC with borderline malignancy (2, 4, 12) and a first case localized in the retrorectal space presenting with system of perianal fistulas.

Item Type: Article
Subjects: Medical and Health Sciences > Clinical medicine
Divisions: Faculty of Medical Science
Depositing User: Ilija Milev
Date Deposited: 11 Sep 2019 06:48
Last Modified: 11 Sep 2019 06:48

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